Volume 6, Number 6—December 2000
Synopsis
Hemophagocytic Syndromes and Infection
Table
Clinical sign | % of patients affected | Reference |
---|---|---|
Fever* | 60-100 | 5,18-21 |
Splenomegaly* | 35-100 | 5,19-21 |
Hepatomegaly | 39-97 | 5,19-21 |
Lymphadenopathy | 17-52 | 5,18-21 |
Rash | 3-65 | 5,18-21 |
Neurologic signs | 7-47 | 19,21 |
Laboratory abnormality | % | Reference |
Anemia* | 89-100 | 5,19,20 |
Thrombocytopenia* | 82-100 | 5,19,20 |
Neutropenia* | 58-87 | 5,19,21 |
Hypertriglyceridemia* | 59-100 | 5,19,21 |
Hypofibrinogenemia* | 19-85 | 5,19,21 |
Hyperbilirubinemia | 74 | 19 |
*Proposed diagnostic criterion for HLH (2)
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