Volume 12, Number 10—October 2006
Research
Human Prion Disease and Relative Risk Associated with Chronic Wasting Disease
Table A1
ICD-9 code classifications for expanded event definition, 1979–1998
| Code definition | Age at death, y | ICD-9 | Total with code* (12–55 y)† |
|---|---|---|---|
| Slow virus infection of the central nervous system | >12 | 046 | 0 (0) |
| Creutzfeldt-Jakob disease | >12 | 046.1 | 54 (8) |
| Other slow virus infection | >12 | 046.8 | 0 (0) |
| Unspecified slow virus infection | >12 | 046.9 | 0 (0) |
| Presenile dementia | 12–55 | 290.1 | 8 (8) |
| Senile dementia, depressed or paranoid type | 12–55 | 290.2 | 0 (0) |
| Cognitive or personality change of other type | >12 | 310.1 | 0 (0) |
| Other cerebral degenerations | >12 | 331 | 0 (0) |
| Alzheimer disease | 12–55 | 331.0 | 18 (18) |
| Pick disease | >12 | 331.1 | 19 (3) |
| Senile degeneration of the brain | >12 | 331.2 | 55 (0) |
| Other cerebral degeneration | >12 | 331.8 | 13 (8) |
| Other cerebral degeneration, unspecified | >12 | 331.9 | 569 (35) |
| Other extrapyramidal disease and abnormal movement disorders | >12 | 333 | 0 (0) |
| Other degenerative diseases of the basal ganglia | >12 | 333.0 | 78 (8) |
| Myoclonus | >12 | 333.2 | 4 (1) |
| Other choreas | >12 | 333.5 | 11 (0) |
| Other and unspecified conditions | >12 | 333.9 | 22 (1) |
| Spinocerebellar disease | >12 | 334 | 0 (0) |
| Primary cerebellar degeneration | >12 | 334.2 | 7 (0) |
| Other cerebellar ataxia | >12 | 334.3 | 18 (1) |
| Cerebellar ataxia in diseases classified elsewhere | >12 | 334.4 | 0 (0) |
| Other spinocerebellar disease | >12 | 334.8 | 27 (6) |
| Unspecified spinocerebellar disease | >12 | 334.9 | 66 (6) |
| Encephalopathy, unspecified | >12 | 348.3 | 620 (183) |
| Sleep disturbances | >12 | 780.5 | 7 (1) |
| Abnormal involuntary movements | >12 | 781.0 | 22 (2) |
| Abnormality of gait | >12 | 781.2 | 13 (1) |
| Lack of coordination | >12 | 781.3 | 49 (0) |
*Deaths may have more than 1 code reported.
†Total deaths with code for persons ages 12–55 y.
